Schwannoma is a well-defined benign tumor which arises from neural crest cells and surround the nerve sheath. Schwannoma of the pancreas is extremely rare, and only a limited number of cases have been reported in the literature as of today. Schwannomas of the pancreatic tail are extremely rare (4%). We hereby report a case of a patient undergoing distal pancreatectomy with en-bloc splenectomy for a cystic lesion of the pancreatic tail. The diagnosis of a pancreatic schwannoma was made upon histological examination.
