Pancreatoblastoma (PBL) is a very rare childhood tumour that develops from pancreatic epithelial exocrine cells. It is the most common malignant pancreatic tumour in children under the age of five, with a mean age of diagnosis of five years. It grows slowly, and its appearance is varied and frequently non-specific. If the tumour is resectable, the prognosis for paediatric cases is usually good, but recurrences do occur. PBL has an aggressive course and a poor prognosis if it is unresectable and has metastasis. Adult cases typically have a shorter survival time, with a median survival time of 15 months. Awareness of this rare pancreatic tumour is critical for early detection and management.
Published Date: 2022-08-25; Received Date: 2022-07-27
