Periodontics and Prosthodontics Open Access

Department of Dentistry, Riyadh Elm University, Saudi Arabia

Publications

• Case Report   
  Dental Management for Patient with Mondini Syndrome
  Author(s): Badria Al Matrafi*, Mohammad Al Sughyer, Saud Al Saif, Majeed Al Jadeed, Sahar Mansour, Saleh Al Garzai, Abdullah Al Eiss and Reem Al Moslem
  
  Mondini syndrome is a rare congenital sensorineural deafness. Malformation of cochlea in inner ear is unilateral or bilateral. May cause hear loss, recurrent meningitis and otorrhea. Mondini syndrome can be isolated or combined with other ear malformation or other syndrome. The condition occurs at seventh week of embryonic development. We report 4 years old female child come to our dental clinic diagnosed with profound hearing loss bilateral with sever mondini deformity in the inner ear, status post brainstem implant done in Germany. Patient is not responding to any sounds. There is no history of any other congenital problems. There is positive history of consanguinity and there is no family history of congenital hearing loss. No history of trauma or meningitis, no significant perinatal history. The patient looks well, no dysmorphic features, normal external audit.. View More»
  

  DOI: 10.36648/2471-3082.8.2.101

  Abstract HTML PDF